Membrane organization of the dystrophin-glycoprotein complex

Cell. 1991 Sep 20;66(6):1121-31. doi: 10.1016/0092-8674(91)90035-w.

Abstract

The stoichiometry, cellular location, glycosylation, and hydrophobic properties of the components in the dystrophin-glycoprotein complex were examined. The 156, 59, 50, 43, and 35 kd dystrophin-associated proteins each possess unique antigenic determinants, enrich quantitatively with dystrophin, and were localized to the skeletal muscle sarcolemma. The 156, 50, 43, and 35 kd dystrophin-associated proteins contained Asn-linked oligosaccharides. The 156 kd dystrophin-associated glycoprotein contained terminally sialylated Ser/Thr-linked oligosaccharides. Dystrophin, the 156 kd, and the 59 kd dystrophin-associated proteins were found to be peripheral membrane proteins, while the 50 kd, 43 kd, and 35 kd dystrophin-associated glycoproteins and the 25 kd dystrophin-associated protein were confirmed as integral membrane proteins. These results demonstrate that dystrophin and its 59 kd associated protein are cytoskeletal elements that are tightly linked to a 156 kd extracellular glycoprotein by way of a complex of transmembrane proteins.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Actins / metabolism
  • Animals
  • Antibodies, Monoclonal
  • Cytoskeleton / ultrastructure
  • Dystrophin / chemistry
  • Dystrophin / physiology*
  • Fluorescent Antibody Technique
  • Glycoproteins / chemistry
  • Glycoproteins / physiology*
  • Glycoside Hydrolases / pharmacology
  • Hydrogen-Ion Concentration
  • Macromolecular Substances
  • Molecular Weight
  • Muscle Proteins / physiology*
  • Neuraminidase / pharmacology
  • Rabbits
  • Sarcolemma / ultrastructure*
  • Solubility

Substances

  • Actins
  • Antibodies, Monoclonal
  • Dystrophin
  • Glycoproteins
  • Macromolecular Substances
  • Muscle Proteins
  • Glycoside Hydrolases
  • Neuraminidase