ReviewRetinitis pigmentosa
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Cited by (116)
Theoretical study on the isomerization process of retinal in gas and aqueous phase
2018, Computational and Theoretical ChemistryCitation Excerpt :Scotopic and photopic visions mediated by the rod and cone cells, respectively, have the characteristics of spectral tuning, disparate sensitivity, and recovery following exposure to light [4–6]. The occurrence of vitamin A in the eye tissues [7] is significant because it is functionally associated with vision, it was well known that absence of carotenoids in a diet lacking retinoid could lead to progressive retinal degeneration [8] and blindness. In the first step of vision (Fig. 1), photoreceptors are activated when light induces the isomerization of 11-cis retinal to all-trans retinal [9,10].
Prevalence, Age at Diagnosis, Mortality, and Cause of Death in Retinitis Pigmentosa in Korea—A Nationwide Population-based Study
2017, American Journal of OphthalmologyWhole-eye electrical stimulation therapy preserves visual function and structure in P23H-1 rats
2016, Experimental Eye ResearchCitation Excerpt :WES therapy offered significant preservation of nuclei in the RGC layer of the P23H-1 rat, a rodent model of RP. A spectrum of inheritable degenerative retina disorders, retinitis pigmentosa is a prominent and incurable cause of human blindness characterized by a progressive loss of rod photoreceptors, followed by cones (Merin and Auerbach, 1976; Wenzel et al., 2005; Yu et al., 2004). While several genes have been implicated to cause RP, approximately 30–40% can be attributed to genetic rhodopsin defects such as the P23H mutation (Ferrari et al., 2011).
Retinal Dystrophy Associated With RLBP1 Retinitis Pigmentosa: A Five-Year Prospective Natural History Study
2023, Investigative Ophthalmology and Visual ScienceOCT-measured retinal vasculature and intrinsic optical responses to transcorneal electrical stimulation
2023, Proceedings of SPIE - The International Society for Optical EngineeringClinical Evaluation of Patients with Retinitis Pigmentosa
2023, Methods in Molecular Biology