Abstract.
A 40-year-old white man with a 3-year history of mild to severe right thigh and knee pain was referred for radiographic investigation. Radiographs show a fusiform, bilaterally symmetrical enlargement of the diaphyses and metaphyses of the long bones (femur, tibia, fibula, radius and ulna). A narrowed medullary cavity is illustrated on CT scan of the femur. All bones show periosteal and endosteal bone formation. There is no history of familial involvement, trauma, infection or systemic illness. Blood chemistry could not point out any abnormality. Radiographic findings and clinical history suggest the diagnosis of Camurati-Engelmann disease, also known as progressive diaphyseal dysplasia (PDD). This case is of interest because of its rare metaphyseal involvement, mild form and sporadic presentation.
Similar content being viewed by others
Author information
Authors and Affiliations
Additional information
Received: 4 December 1997; Revision received: 3 March 1998; Accepted: 5 March 1998
Rights and permissions
About this article
Cite this article
Brat, H., Hamoir, X., Matthijs, P. et al. Camurati-Engelmann disease: a late and sporadic case with metaphyseal involvement. Eur Radiol 9, 159–162 (1999). https://doi.org/10.1007/s003300050648
Issue Date:
DOI: https://doi.org/10.1007/s003300050648