Table 2

Cochlear implant outcomes in TMPRSS3-associated hearing loss (bold) and the general hearing loss population

StudySubjects (n)Preoperative CNC WRS, %14 Postoperative CNC WRS, %14
This study 30 17.4 (15.3) 66.2 (25.8)
Kelsall et al 27 10014.6 (11.6)65.2 (18.8)
Sullivan et al 32 608.4 (19)33
Pillsbury et al 26 7330.4 (13.4)66.9 (18.5)
Cusumano et al 31 266.6 (10.1)42.1 (33.2)
O’Connell et al 28 220n/a46.6 (23.0)
Kamakura and Nadol30 17n/a40.3 (19.4)
Buchman et al 25 13060
Zwolan et al 29 562.25 (3.95)42.2 (23.5)
  • CNC, consonant-nucleus-consonant; n/a, not available; WRS, word recognition scores.