Table 1

Mitochondrial respiratory chain assay from fibroblasts and muscle

MRC from fibroblastsPer cent of control (%)Absolute values (mU/U CS)Reference range (Mean±SD)Range
F1 II-1F1 II-2F1 II-1F1 II-2
I342014788(433±85)237–618
II8982487447(545±97)364–826
II+III6272327381(526±133)298–795
III123112116105(94±27)32–143
IV77981519(19±5)13–35
MRC from muscle of F1 Ⅱ-1 Per cent of control Absolute values (mU/U CS) Reference range
(Mean±SD)
Range
(%)
I2482(346±38)279–405
II91285(313±55)209–425
II+III103308(299±98)131–488
III108186(172±71)53–296
IV17152(31±13)20–62
  • MRC, mitochondrial respiratory chain.