Mitochondrial respiratory chain assay from fibroblasts and muscle
| MRC from fibroblasts | Per cent of control (%) | Absolute values (mU/U CS) | Reference range (Mean±SD) | Range | ||
| F1 II-1 | F1 II-2 | F1 II-1 | F1 II-2 | |||
| I | 34 | 20 | 147 | 88 | (433±85) | 237–618 |
| II | 89 | 82 | 487 | 447 | (545±97) | 364–826 |
| II+III | 62 | 72 | 327 | 381 | (526±133) | 298–795 |
| III | 123 | 112 | 116 | 105 | (94±27) | 32–143 |
| IV | 77 | 98 | 15 | 19 | (19±5) | 13–35 |
| MRC from muscle of F1 Ⅱ-1 | Per cent of control | Absolute values (mU/U CS) | Reference range (Mean±SD) | Range | ||
| (%) | ||||||
| I | 24 | 82 | (346±38) | 279–405 | ||
| II | 91 | 285 | (313±55) | 209–425 | ||
| II+III | 103 | 308 | (299±98) | 131–488 | ||
| III | 108 | 186 | (172±71) | 53–296 | ||
| IV | 171 | 52 | (31±13) | 20–62 | ||
MRC, mitochondrial respiratory chain.