Classification of dental enamel defects in Loeys-Dietz syndrome (LDS)
| Classification | Description | LDS n=40 | Unaffected n=26 |
| Grade 0 | Normal enamel | 18 (45.0) | 20 (76.9) |
| Grade 1 | Tooth discolouration: white, yellow or brown spots on smooth enamel surfaces | 14 (35.0) | 6 (23.1) |
| Grade 2 | Localised <2/3 of structural defects: <6 teeth affected | 3 (7.5) | 0 (0.0) |
| Grade 3 | Localised ≥2/3 of structural defects: <12 teeth affected | 3 (7.5) | 0 (0.0) |
| Grade 4 | Generalised structural defects: affect the whole dentition | 2 (5.0) | 0 (0.0) |
Frequencies of each grade are mentioned along with the percentage within the category in parenthesis.