Table 3

Classification of dental enamel defects in Loeys-Dietz syndrome (LDS)

ClassificationDescriptionLDS
n=40
Unaffected
n=26
Grade 0Normal enamel18 (45.0)20 (76.9)
Grade 1Tooth discolouration: white, yellow or brown spots on smooth enamel surfaces14 (35.0)6 (23.1)
Grade 2Localised <2/3 of structural defects: <6 teeth affected3 (7.5)0 (0.0)
Grade 3Localised ≥2/3 of structural defects: <12 teeth affected3 (7.5)0 (0.0)
Grade 4Generalised structural defects: affect the whole dentition2 (5.0)0 (0.0)
  • Frequencies of each grade are mentioned along with the percentage within the category in parenthesis.