Infections | Patient P1 | Patient P2 | Patient P3 | Patient P6 | Patient P7 | Patient P8 |
---|---|---|---|---|---|---|
Candidiasis | ||||||
Oral | 6 month | 12 month | 12 month | 13 month | 2 month | Since birth |
Nail (and skin) | 5 year | 3 year | 12 year | 4,5 year | 1 year | 3 month |
Oesophageal | no | 19 year | no | 8 year | 6 year | 5 year |
Genital | no | 8 year | 11 year | no | No | 8 year |
Viral infections | ||||||
Varicella | 8 year | 6 year | 5 year | 5 year | No | 10 year (mild) |
Recurrent HSV infection | no | 20 year | no | no | No | 3 year (6–10 per year) |
Other infections | ||||||
Pneumonia | 3 year (4×) | no | no | 2,5 year (4×) | 5 year | 2 year (4×) |
Aphthous stomatitis | no | 6 year | 6 year | 1 year (3–4×) | 6 month (2–3 yearly, >4r | 2 month (monthly) |
Furunculosis | no | no | no | 7 year (>3 per year) | – | 6 year (3×) |
Impetigo | no | no | no | no | no | 5 year (1–2 per year) |
Blepharitis | 8 year (1) | no | no | no | no | 5 year (6×) |
Keratitis | No | 5 year | no | no | no | no |
Renal abscess | 9 year | no | no | no | no | no |
Cystitis | no | 20 year | 12 year | 12 year (2×) | no | no |
Periodontitis | no | no | no | 7 year | no | no |
*Age at first episode (times of recurrences); For clinical data of previously published patients (P4, P5 and P9), see online supplementary case reports.
HSV, Herpes simplex virus.