Table 4 Mean (SD) data at entry into the Fabry Outcome Survey according to whether patients were alive or dead at the time of the analysis
Adult femalesAdult males
AliveDeadAliveDead
Proteinuria, mg/24 h324.5 (528.4), n = 3111267.5 (1106.0), n = 5641.6 (967.9), n = 301904.3 (1127.5), n = 18
Serum creatinine, mg/dL0.9 (0.4), n = 4241.2 (0.3), n = 71.6 (1.7), n = 3882.3 (2.3), n = 25
Estimated GFR, mL/min/1.73 m280.6 (21.9), n = 34254.2 (15.1), n = 780.5 (37.0), n = 33572.0 (49.4), n = 22
Midwall fractional shortening, %16.8 (3.4), n = 20411.8 (4.4), n = 615.4 (4.5), n = 13213.8 (3.6), n = 10
LVM, g46.9 (20.1), n = 21886.1 (29.0), n = 654.6 (21.7), n = 15382.1 (38.8), n = 13
FOS–MSSI11.8 (9.0), n = 55826.4 (14.5), n = 717.9 (10.1), n = 49730.7 (12.1), n = 33
Age at entry*, years43.4 (14.3), n = 61361.0 (10.0), n = 738.2 (12.1), n = 54649.8 (9.6), n = 35
Age at death, years64.4 (10.0), n = 751.8 (9.3), n = 35
  • GFR, glomerular filtration rate; LVM, left ventricular mass; FOS–MSSI, Mainz Severity Score Index.

  • *Into the Fabry Outcome Survey.