Adult females | Adult males | |||
Alive | Dead | Alive | Dead | |
Proteinuria, mg/24 h | 324.5 (528.4), n = 311 | 1267.5 (1106.0), n = 5 | 641.6 (967.9), n = 301 | 904.3 (1127.5), n = 18 |
Serum creatinine, mg/dL | 0.9 (0.4), n = 424 | 1.2 (0.3), n = 7 | 1.6 (1.7), n = 388 | 2.3 (2.3), n = 25 |
Estimated GFR, mL/min/1.73 m2 | 80.6 (21.9), n = 342 | 54.2 (15.1), n = 7 | 80.5 (37.0), n = 335 | 72.0 (49.4), n = 22 |
Midwall fractional shortening, % | 16.8 (3.4), n = 204 | 11.8 (4.4), n = 6 | 15.4 (4.5), n = 132 | 13.8 (3.6), n = 10 |
LVM, g | 46.9 (20.1), n = 218 | 86.1 (29.0), n = 6 | 54.6 (21.7), n = 153 | 82.1 (38.8), n = 13 |
FOS–MSSI | 11.8 (9.0), n = 558 | 26.4 (14.5), n = 7 | 17.9 (10.1), n = 497 | 30.7 (12.1), n = 33 |
Age at entry*, years | 43.4 (14.3), n = 613 | 61.0 (10.0), n = 7 | 38.2 (12.1), n = 546 | 49.8 (9.6), n = 35 |
Age at death, years | – | 64.4 (10.0), n = 7 | – | 51.8 (9.3), n = 35 |
GFR, glomerular filtration rate; LVM, left ventricular mass; FOS–MSSI, Mainz Severity Score Index.
*Into the Fabry Outcome Survey.