| Cause of death | Received ERT at some time | Never received ERT | Overall | ||||||
| M | F | Total | M | F | Total | M | F | Total | |
| Cardiac | 10 | 2 | 12 | 2 | 2 | 4 | 12 | 4 | 16 |
| Renal | 3 | 0 | 3 | 0 | 0 | 0 | 3 | 0 | 3 |
| Cerebrovascular | 3 | 0 | 3 | 1 | 0 | 1 | 4 | 0 | 4 |
| Respiratory | 2 | 0 | 2 | 1 | 0 | 1 | 3 | 0 | 3 |
| Malignancy | 1 | 1 | 2 | 1 | 0 | 1 | 2 | 1 | 3 |
| Infection | 5 | 0 | 5 | 0 | 0 | 0 | 5 | 0 | 5 |
| Multisystemic | 2 | 2 | 4 | 2 | 0 | 2 | 4 | 2 | 6 |
| Other | 2 | 0 | 2 | 0 | 0 | 0 | 2 | 0 | 2 |
| Total | 28 | 5 | 33 | 7 | 2 | 9 | 35 | 7 | 42 |
ERT, enzyme-replacement therapy.
Data on patients who had received ERT at some point before death were available during the period between 2001 and 2007, and information on deaths of patients who never received ERT could be added from August 2006 onwards.