Patients, n | Prevalence/10 000 births | Anotia, % | Isolated, % | Unilateral, % | Laterality | Sex ratio | Aural atresia or stenosis, % | Other clinical abnormalities, % | Familial, % | Origin of patients | Ref. |
80 | 17.4 | — | 85 | 93 | 67% R | — | — | — | 15 | Quito, Ecuador | 2 |
175 | 3.2 | — | 66 | 90 | 60% R | — | — | — | — | South America | |
294 | — | 61 | 70% R | 64% M | — | 45 | — | Chicago, USA | 7 | ||
172 | 1.5 | — | 66 | 85 | 57% R | — | 44 | — | Italy | 14 | |
954 | 0.8 | 45 | 68 | — | — | — | — | — | — | Central/eastern France | 4 |
2.4 | 9 | 67 | — | 61% R | M>F | — | — | — | Sweden | ||
2 | 2 | 50 | — | — | — | — | — | — | California, USA | ||
592 | — | — | — | 91 | 64% R | 65% M | 92 | 3 | Japan | 9 | |
38 | 3.8 | — | — | 81 | R more common | 63% M | — | 53 | 15 | Venezuela | 5 |
145 | — | — | — | 75 | 52% R | 60% M | 55 | 25 | 34 | Mexico City, Mexico | 12 |
453 | 1.4 | — | — | — | — | No sex difference | — | 60 | — | China | 11 |
636 | 2.2 | — | 25 | 79 | — | M>F | — | — | — | California, USA | 8 |
120 | 3.8 | 8 | 56 | 80 | 64% R | M>F | — | — | — | Hawaii, USA | 3 |
53 | — | — | — | 49 | 46% R | 60% M | — | — | 9,4 | Germany | 43 |
190 | 4.3 | 5 | 67 | 88 | 60% R | 58% M | 93 | — | 20 | Finland | 6 |
M, Male; F, Female; R, Right; Ref, Reference.