Patient no | Age, years | Heart disease | Hyper-tension | Karyotype | Outcome | Pathology | Location of dissection | Other information | CHD exclusion criteria | Reference | ||||||||||
1 | 20 | No | No | 45,X | Deceased | CMN | Proximal | NR | Rubin55 | |||||||||||
2 | 27 | No | No | NR | Alive | NR | Very distal | Abdominal aorta | Echo, angiography, MRI | Bartlema56 | ||||||||||
3 | 30 | No | No | 45X/46X + ring | Deceased | CMN | Proximal | Autopsy | Price57 | |||||||||||
4 | 39 | No | No | 45,X | Deceased | NR | Proximal and distal | Autopsy | Price57 | |||||||||||
5 | 51 | No | No | 45,X/46 X, r(X) | Alive | NR | Proximal | NR | Gravholt1 | |||||||||||
6 | 53 | No | No | 45,X | Deceased | NR | Proximal | NR | Gravholt1 | |||||||||||
7 | NR | No | No | NR | Deceased | NR | NR | Dissection during third trimester of pregnancy | NR | Nagel40 | ||||||||||
8 | 9.5 | NR | No | 45,X | Alive | NR | Site of surgical repair? | NR | Sybert2 | |||||||||||
9 | 10 | No | NR | NR | Deceased | NR | Proximal | NR | Hata58 | |||||||||||
10 | 18 | NR | NR | 45 X/46XY | Deceased | CMN | Proximal | NR | Gravholt1 | |||||||||||
11 | 28 | NR | No | 45,X | Deceased | NR | Distal | NR | Gravholt1 | |||||||||||
12 | 29 | No | NR | 45,X/46X,r(X) | Deceased | NR | NR | Price59 | ||||||||||||
13 | 30 | NR | NR | NR | Alive | NR | Proximal | Surgical repair | NR | Hirose60 | ||||||||||
14 | 34 | NR | NR | NR | NR | NR | NR | Dissection of aortic aneurysm | NR | Chlumsky61 | ||||||||||
15 | 38 | NR | NR | 45,X | Alive | NR | Proximal | Surgical repair | NR | Meunier62 | ||||||||||
16 | NR | NR | NR | Alive | NR | Distal | NR | Clement63 | ||||||||||||
17 | 39 | No | NR | 45,X | Deceased | NR | NR | NR | Price59 | |||||||||||
18 | 49 | No | NR | NR | Deceased | NR | NR | NR | Hata58 | |||||||||||
19 | 61 | NR | No | 45,X | Deceased | NR | NR | NR | Gravholt1 |
AI, aortic insufficiency; AS, aortic stenosis; BAV, bicuspid aortic valve; BE, subacute bacterial endocarditis; CMN, cystic medial necrosis; LCA, left coronary artery; NR, not reported; SCHD, coronary heart disease.