Table 1

 Biochemical activities*

Complex I/CS†Complex II+III/CSComplex IV/CSCitrate synthase
*nM/min/mg protein; nv, normal values; †citrate synthase.
Muscle10.4 (nv 15±4)9.5 (nv 12±3)46 (nv 106±28)82 (nv 133±27)
Fibroblasts31 (nv 140±27)140 (nv 150±25)