Table 2

Enzyme activities of heparan-N-sulphatase, acetyl-CoA N-acetyl transferase, α-N-acetylglucosaminidase, and N-acetylglucosamine-6-sulphatase in the patient and controls

Cell typeEnzymeUnitsPatientControls
LeucocytesHeparan-N-sulphatasepmol/h/mg protein280265 & 168
LeucocytesAcetyl-CoA N-acetyl transferasenmol/h/mg protein2.40.64–4.2
Plasmaα-N-acetyl-glucosaminidasenmol/h/mg protein4012–73
FibroblastsN-acetylglucosamine-6-sulphatasenmol/17h/mg protein091–138