Diagnostic criteria for NF2
| A diagnosis of NF2 is made in a patient who has (NIH criteria, 1987): |
| Bilateral vestibular schwannomas |
| OR family history of NF2 |
| PLUS unilateral vestibular schwannoma |
| OR any two of: meningioma, glioma, neurofibroma, schwannoma, posterior subcapsular lenticular opacities |
| A diagnosis of NF2 can also be made in a patient who has (Evans et al6): |
| Unilateral vestibular schwannoma |
| PLUS any two of: meningioma, glioma, neurofibroma, schwannoma, posterior subcapsular lenticular opacities |
| OR multiple meningiomas (2 or more) |
| PLUS unilateral vestibular schwannoma |
| OR any two of: glioma, neurofibroma, schwannoma, cataract |