Table 1

Phenotypic evaluation of deaf subjects in the family

Audiogram*Exposure to
SubjectsAgeGenderSeverityShapeAminoglycosideNoise
*Audiograms were categorised based on the classification of Liu and Xu.8
†Caloric testing was performed.
III.973MSevereFlat
III.1171FSevereFlat
IV.254FModerateFlat
IV.9†60MSevereFlatYes
IV.1263FSevereFlat
IV.13†56FModerateFlat
IV.15†54MSevereFlat
IV.17†49MSevereFlat
IV.19†43FSevereAscending
V.130FModerateAscendingYes
V.218FMildAscending
V.3†14MModerateFlat
V.431MSevereSloping
V.5†30FSevereAscending
V.728MModerateSlopingYes
V.11†28FModerateAscending
V.12†33MSevereSlopingYes
V.1428MModerateSloping
V.15†18MModerateSloping
V.1614FModerateAscendingYes
VI.212FModerateAscending