Table 1

Current clinical evaluation of some members of the pedigree

SubjectAge at onsetDeafnessDental alterationsBone alterations
II.112+++++++++
II.312+++++++++
II.411+++++++++
II.513+++++++++
II.613+++++++++
III.135++
III.512++
III.920+++
III.1020++++++
III.1111+++++
III.1215+++++++
III.1310+++++
III.1410+++
III.1615+
IV.117+
IV.312+
IV.413+
IV.1212+++
IV.1411+++
IV.1711+
IV.1810+
IV.207+++