Biochemical analysis of respiratory chain complexes I, II+III, and IV, and PDHC in muscle tissue
| Muscle activity (mU/U CS) | |||
|---|---|---|---|
| Patient | Control range | ||
| PDHC | 9.3 | 20–52 | |
| NADH:Q1 oxidoreductase (CI) | 60 | 170–560 | |
| Succinate:cyt C oxidoreductase (CII+III) | 70 | 80–450 | |
| Cytochrome C oxidase (CIV) | 1370 | 900–4700 | |
| Citrate synthase | 75.0 | 45–1051-150 | |
↵1-150 Citrate synthase (CS) in U/g NCP.