Diagnostic criteria for NF2 (these include the NIH criteria8 with additional criteria21)
| Bilateral vestibular schwannomas orfamily history of NF2 plus |
|---|
| (1) Unilateral VS or |
| (2) Any two of: meningioma, glioma, neurofibroma, schwannoma, posterior subcapsular lenticular opacities |
| Additional criteria |
| Unilateral VS plusany two of: meningioma, glioma, neurofibroma, schwannoma, and posterior subcapsular opacities |
| or |
| Multiple meningioma (two or more) plusunilateral VS or any two of: glioma, neurofibroma, schwannoma, and cataract |
“Any two of” refers to individual tumours or cataract, not to tumour types.