Table 1

Summary of diagnostic features of affected subjects

ID	Sinusitis	Documented bronchiectasis	Ciliary dysmotility	Ultrastructural defect by EM	Situs inversus	Sweat Na (mmol/l)	Normal immunoglobulins
65 II.3	+	−	NA	NA	+	NA	NA
65 II.4	+	+	+	NA	−	29	+
66 III.2	+	+	+	NA	−	54, 15	NA
66 III.3	+	−	+	NA	−	46	NA
67 II.3	+	+	+	NA	+	14	+
67 II.4	+	NA	NA	NA	+	NA	NA
69 II.4	+	−	+	NA	−	40, 42	+
72 II.3	+	+	+	+	+	NA	+
89 II.1	+	+	+	+	−	Normal	+
89 II.2	+	+	+	+	+	Normal	+
89 II.3	+	+	+	+	−	Normal	+

+, present; −, absent; NA, not available; Normal, as documented from clinical notes of referring physician.