Table 2

Protein components of fibrillin-containing associated microfibrils

No Protein Localisation Exons Size Remarks
115 22 Fibrillin-115q15-2165350 kDa, 2871 amino acidsRGD motif
232 Fibrillin-25q23-q3165350 kDa2 RGD motifs
373 195 MAGP-1 (MFAP-2)1p36931 kDa13 cysteine residues
477 MAGP-212p12.3-12p13.2925 kDa; 173 amino acidsRGD motif
581 82 MFAP-115q15-q219439 amino acids22% glutamic acid
684 MFAP-35q32-q33.22362 amino acids23% glutamic acid; 6% aspartic acid
786 87 MFAP-417p11.2?36 kDa; 255 amino acidsRGD motif
888 AAAP-40, rAAAP-CL4???Not yet well characterised
  • MAGP = microfibril associated glycoprotein; MFAP = microfibril associated protein; AAAP-40 = aortic aneurysm associated protein-40.