Diagnostic criteria for NF2
Bilateral vestibular schwannomas OR family history of NF2 PLUS |
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(1) Unilateral VS OR |
(2) Any two of: meningioma, glioma, neurofibroma, schwannoma, posterior subcapsular lenticular opacities |
Additional criteria |
Unilateral VS + any two of: meningioma, glioma, neurofibroma, schwannoma, and posterior subcapsular opacities |
OR |
Multiple meningioma (2 or more) + unilateral VS or any 2 of: glioma, neurofibroma, schwannoma, and cataract |