Health related quality of life (carriers v non-carriers v uncertain)
| RAND dimension | Mean scores (SD) | p value | |||
|---|---|---|---|---|---|
| Carrier (n=5) | Non-carrier (n=7) | Uncertain (n=11) | |||
| Duchenne muscular dystrophy | |||||
| Physical functioning | 98.0 (4.5) | 95.0 (13.2) | 99.5 (1.6) | 0.513 | |
| Physical role functioning | 100 | 89.3 (28.3) | 93.2 (16.2) | 0.642 | |
| Energy/fatigue | 77.0 (14.0) | 72.9 (9.9) | 62.7 (18.4) | 0.190 | |
| Emotional role functioning | 100 | 90.5 (25.2) | 81.8 (31.1) | 0.433 | |
| Emotional well being | 83.2 (13.1) | 79.4 (10.7) | 74.5 (13.3) | 0.425 | |
| Social functioning | 93.8 (12.5) | 92.9 (12.2) | 92.0 (12.8) | 0.972 | |
| Bodily pain | 86.0 (15.2) | 94.3 (7.9) | 88.1 (12.5) | 0.445 | |
| General health | 82.0 (22.8) | 79.3 (10.6) | 80.0 (13.7) | 0.953 | |
| Carrier (n=2) | Non-carrier (n=10) | Uncertain (n=11) | p value | ||
| Haemophilia A | |||||
| Physical functioning | 100 | 97.5 (5.4) | 98.2 (3.4) | 0.753 | |
| Physical role functioning | 87.5 (17.7) | 87.5 (31.7) | 86.4 (32.3) | 0.996 | |
| Emotional role functioning | 100 | 86.7 (32.2) | 93.3 (21.1) | 0.753 | |
| Energy/fatigue | 75.0 (7.0) | 78.5 (12.3) | 68.2 (17.8) | 0.312 | |
| Emotional well being | 80.0 (5.7) | 86.4 (5.1) | 74.5 (17.9) | 0.146 | |
| Social functioning | 81.3 (8.8) | 91.3 (10.3) | 90.9 (13.8) | 0.557 | |
| Bodily pain | 80.0 (14.1) | 95.0 (10.8) | 80.0 (22,8) | 0.165 | |
| General health | 82.5 (3.5) | 77.5 (14.0) | 77.7 (21.0) | 0.932 | |
Analysis of variance, p<0.01.