Table 2

Frequency of transmission of the larger and smaller alleles at dentatorubral-pallidoluysian atrophy disease locus

MeiosisAllele transmittedχ2assuming 1:1 segregationp (χ2)
LargerSmallerNot informativeTotal typed
MZ
 Paternal353019840.1340.714
 Maternal3232349801
DZ
 Paternal9287752540.1400.709
 Maternal102119742951.3080.253
Total
 Paternal127117943380.4100.522
 Maternal1341511083931.0140.314