[HTML][HTML] Lung clearance index: evidence for use in clinical trials in cystic fibrosis

L Kent, P Reix, JA Innes, S Zielen, M Le Bourgeois… - Journal of Cystic …, 2014 - Elsevier
Abstract The ECFS-CTN Standardisation Committee has undertaken this review of lung
clearance index as part of the group's work on evaluation of clinical endpoints with regard to …

Autosomal dominant STAT3 deficiency and hyper-IgE syndrome: molecular, cellular, and clinical features from a French national survey

…, N Mahlaoui, S Blanche, M Debré, M Le Bourgeois… - Medicine, 2012 - journals.lww.com
Autosomal dominant deficiency of signal transducer and activator of transcription 3 (STAT3)
is the main genetic etiology of hyper-immunoglobulin (Ig) E syndrome. We documented the …

Allergy to betalactam antibiotics in children: results of a 20‐year study based on clinical history, skin and challenge tests

…, A Bados‐Albiero, M Le Bourgeois… - Pediatric Allergy and …, 2011 - Wiley Online Library
To cite this article: Ponvert C, Perrin Y, Bados‐Albiero A, Le Bourgeois M, Karila C,
Delacourt C, Scheinmann P, De Blic J. Allergy to betalactam antibiotics in children: results of …

Efficacy of the Janus kinase 1/2 inhibitor ruxolitinib in the treatment of vasculopathy associated with TMEM173-activating mutations in 3 children

…, M Fabre, L Berteloot, M Le Bourgeois… - Journal of Allergy and …, 2016 - jacionline.org
Efficacy of the Janus kinase 1/2 inhibitor ruxolitinib in the treatment of vasculopathy
associated with TMEM173-activating mutat and has received grants from the National …

Matrix-assisted laser desorption ionization-time of flight mass spectrometry for identification of nonfermenting gram-negative bacilli isolated from cystic fibrosis patients

…, B Dauphin, JL Beretti, M Le Bourgeois… - Journal of clinical …, 2008 - Am Soc Microbiol
The identification of nonfermenting gram-negative bacilli isolated from cystic fibrosis (CF)
patients is usually achieved by using phenotype-based techniques and eventually …

Microbiological diagnosis of empyema in children: comparative evaluations by culture, polymerase chain reaction, and pneumococcal antigen detection in pleural …

…, JR Zahar, M Le Bourgeois… - Clinical infectious …, 2006 - academic.oup.com
Background. Pleural empyema is an increasingly reported complication of pneumonia in
children. Microbiological diagnostic tests for empyema by culture frequently have false …

[HTML][HTML] Mycobacterium abscessus and children with cystic fibrosis

I Sermet-Gaudelus, M Le Bourgeois… - Emerging infectious …, 2003 - ncbi.nlm.nih.gov
We prospectively studied 298 patients with cystic fibrosis (mean age 11.3 years; range 2
months to 32 years; sex ratio, 0.47) for nontuberculous mycobacteria in respiratory samples …

Age-related prevalence and distribution of nontuberculous mycobacterial species among patients with cystic fibrosis

…, I Sermet-Gaudelus, M Le Bourgeois… - Journal of clinical …, 2005 - Am Soc Microbiol
We studied the prevalence and species distribution of nontuberculous mycobacteria (NTM)
in relation to age in 385 patients with cystic fibrosis (CF)(mean age±standard deviation …

Long-term outcome of idiopathic pulmonary hemosiderosis in children

L Le Clainche, M Le Bourgeois, B Fauroux, N Forenza… - Medicine, 2000 - journals.lww.com
Long-Term Outcome of Idiopathic Pulmonary Hemosiderosis in C... : Medicine Long-Term
Outcome of Idiopathic Pulmonary Hemosiderosis in Children : Medicine Log in or Register Get …

The French compassionate programme of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis with advanced lung disease and no F508del CFTR variant

…, I Fajac, I Honoré, M Le Bourgeois… - European …, 2023 - Eur Respiratory Soc
Background The European Medicines Agency has approved the cystic fibrosis
transmembrane conductance regulator (CFTR) modulator combination …