Table 1

 Scores and centile performance (age corrected) for verbal IQ, memory and executive skills tests

SubjectAge (years)VIQVocabularySimilaritiesDigit spanVerbal recall immediateVerbal recall %Verbal learning trialsVerbal learning: delayFluency phonemic “s”Fluency animalsHayling total scoreCognitive estimates
The genealogical relationships among subjects are shown in fig 1.
Affected
II:282117 (84th)14121526 (25th)92 (25th)31 (10th)6 (25th)2519 (75th)13 (10th)1
II:675117 (84th)14131324 (25th)83 (25th)40 (25th)9 (50th)1918 (75th)14 (10th)3
II:860113 (75th)11101729 (25th)100 (75th)50 (50th)9 (25th)2517 (50th)19 (50th)1
III:153150 (99th)18161841 (75th)90 (25th)55 (50th)15 (90th)3030 (90th)20 (75th)0
III:249146 (99th)16161629 (25th)79 (10th)64 (90th)12 (50th)2836 (90th)22 (95th)0
III:554129 (98th)14141538 (50th)95 (50th)58 (50th)13 (75th)3031 (90th)19 (50th)2
IV:219112 (75th)10121127 (25th)107 (90th)62 (75th)13 (75th)1621 (50th)19 (50th)6
IV:338134 (98th)12151452 (90th)96 (75th)54 (50th)13 (75th)1821 (50th)21 (90th)2
Unaffected
II:481102 (50th)10111125 (25th)80 (25th)36 (10th)7 (25th)2218 (75th)14 (10th)5
III:45792 (25th)8101013 (<1st)77 (10th)33 (<1st)5 (<1st)1518 (25th)17 (50th)4
III:748113 (75th)9111128 (25th)86 (25th)51 (50th)12 (50th)1625 (75th)17 (50th)3
IV:43081 (9th)67728 (25th)94 (50th)41 (<1st)9 (10th)1520 (50th)15 (25th)4
IV:524103 (50th)911138 (50th)95(50th)55 (25th)11 (25th)1723 (50th)12 (5th)7
IV:626101 (50th)9111120 (<1st)95 (50th)36 (<1st)9 (10th)1826 (75th)18 (50th)5
IV:722103 (50th)7121214 (<1st)71 (<1st)49 (25th)10 (25th)1620 (50th)16 (25th)5