Table 1 Patients with no hypertension or congenital heart disease

Patient no	Age, years	Heart disease	Hyper-tension	Karyotype	Outcome	Pathology	Location of dissection	Other information	CHD exclusion criteria	Reference
1	20	No	No	45,X	Deceased	CMN	Proximal		NR	Rubin55
2	27	No	No	NR	Alive	NR	Very distal	Abdominal aorta	Echo, angiography, MRI	Bartlema56
3	30	No	No	45X/46X + ring	Deceased	CMN	Proximal		Autopsy	Price57
4	39	No	No	45,X	Deceased	NR	Proximal and distal		Autopsy	Price57
5	51	No	No	45,X/46 X, r(X)	Alive	NR	Proximal		NR	Gravholt1
6	53	No	No	45,X	Deceased	NR	Proximal		NR	Gravholt1
7	NR	No	No	NR	Deceased	NR	NR	Dissection during third trimester of pregnancy	NR	Nagel40
8	9.5	NR	No	45,X	Alive	NR	Site of surgical repair?		NR	Sybert2
9	10	No	NR	NR	Deceased	NR	Proximal		NR	Hata58
10	18	NR	NR	45 X/46XY	Deceased	CMN	Proximal		NR	Gravholt1
11	28	NR	No	45,X	Deceased	NR	Distal		NR	Gravholt1
12	29	No	NR	45,X/46X,r(X)	Deceased	NR	NR			Price59
13	30	NR	NR	NR	Alive	NR	Proximal	Surgical repair	NR	Hirose60
14	34	NR	NR	NR	NR	NR	NR	Dissection of aortic aneurysm	NR	Chlumsky61
15	38	NR	NR	45,X	Alive	NR	Proximal	Surgical repair	NR	Meunier62
16		NR	NR	NR	Alive	NR	Distal		NR	Clement63
17	39	No	NR	45,X	Deceased	NR	NR		NR	Price59
18	49	No	NR	NR	Deceased	NR	NR		NR	Hata58
19	61	NR	No	45,X	Deceased	NR	NR		NR	Gravholt1

AI, aortic insufficiency; AS, aortic stenosis; BAV, bicuspid aortic valve; BE, subacute bacterial endocarditis; CMN, cystic medial necrosis; LCA, left coronary artery; NR, not reported; SCHD, coronary heart disease.