Table 1

Summary of clinical data for some patrilineal members in the Chinese pedigree

SubjectSexAge of test (years)Age of onset (years)Pure tone audiometry (dB hearing loss), rightPure tone audiometry (dB hearing loss), leftHearing impairment
V-1Male7178580severe
V-5Male55227567moderate
V-7Male63127878severe
V-19Male5487063moderate
V-21Male45279085severe
V-30Male51205660moderate
V-32Male4887877severe
V-34Male4297974severe
VI-3Male2478473severe
VI-8Male3277675severe
VI-10Male35207380severe
VI-26Male23187678severe
VI-27Male2286460moderate
VI-28Male13133528mild
VI-34Male2685864moderate
VI-35Male22186560moderate
VI-36Male1198079severe
VII-5Male978375severe
VII-2Male<1not applicablenot applicablenormal
VII-3Male2not applicablenot applicablenormal
VII-6Male4not applicablenot applicablenormal