Table 3

 Electrophysiological features in eight individuals with neurofibromatosis 1 and neurofibromatous neuropathy

CaseR, L suralR, L suralR, L medianR, L medianR medianR medianR medianR medianL posteriorL posteriorL posteriorL posterior
SAP,µVSCV,m/sSAP,µVSCV,m/sDMAP,mVDML,msMCV,m/sF wave latency,msTibial DMAP,mVTibial DML,msTibial MCV,M/sTibial F wave latency,ms
DMAP, distally evoked compound muscle action potential; DML, distal motor latency; MCV, maximal motor conduction velocity; NA, not available; ND, not done; SAP, sensory action potential; SCV, sensory conduction velocity.
Abnormal figures are given in bold.
1 3, 5 ND, 4514, 1844, 484 4.4 ND 33 55.9ND 61
2 0, 0 NA, NANDNDND 4.6 NDND 0 0NANA
3ND, 5ND, NDND, NDND, NDND 5.2 ND 36 2 9.5 ND 75
4 5, 5 ND, 4620, 944, 44ND 4.3 NDND4.55.3ND57
5 0, 0 NA, NAND, NDND, ND5.5 4.6 ND 36 0 NANANA
68, 5ND, NDNDNA, NDNDNDNDND6.24.66149
7 0, 0 ND, ND11, NDND, NDNDNDNDND 3.4 7.6 ND 63
8 2, 0 ND, NAND, NDND, ND4 4.7 ND 36 NDNDNDND