Patient (see fig 1) | Platelets (×109/l) | Hepatosplenomegaly | Raised liver enzymes (AST/ALT) | IgG/IgM | Rheumatoid factor |
---|---|---|---|---|---|
NK = not known. Serum IgG normal range 0.55–1.8 g/l; IgM normal range 0.05–0.30 g/l . | |||||
XI.8 | 76. Purpura | Yes | Yes | 5.15/1.06 | Negative |
XII.5 | NK | No | No | 1.7/0.21 | Negative |
XII.7 | NK | Yes | No | 1.8/0.47 | NK |
XII.9 | Thrombocytopenia | Yes | NK | 1.4/0.42 | Positive |
XII.12 | Thrombocytopenia, purpura, and bruising | No | No | 16.3/3.6 | NK |
XIII.8 | NK | NK | NK | 3.1/0.17 | 1:1800 |
XIV.3 | 20–35. Required several platelet transfusions | Yes | Yes | 7.29/1.33 | NK |