LMG181 | III-1 | F | 30 | 6 | Moderate to profound | Oral; HA | 10–11 | Good CV; 15° VF | Mild | 1. Endolymphatic shunt 2. Asymmetric hearing loss 3. Cataract surgery |
| II-3 | M | 52 | 5–6 | Mild to moderate | Oral; HA | 9–10 | Light perception, gross objects; minimal VF | None | 1. Cataract surgery |
LMG187 | III-3 | M | 48 | 7–8 | Profound | Oral; CI | 4 | NA | None | 1. Mumps encephalitis at 4 years |
LMG191 | II-1 | M | 50 | Late teens | Moderate to profound | Oral; HA | 5 | Totally blind since 38 years | None | 1. Asymmetric hearing loss |
LMG195 | II-3 | F | 41 | 9–10 | Mild to severe | Oral; HA | 10 | 20/60; good CV; <5° VF | None (normal) | 1. Cataract surgery 2. Otospongiosus at 20–30 years |
| II-2 | F | 44 | 3 | Severe to profound | Oral; HA | 12 | 20/70; good CV; 15°VF | Mild (normal at 14 years) | 1. Cataract surgery 2. Endolymphatic shunt at ~20 years |
LMG198 | II-3 | F | 40 | 9–10 | Severe | Oral; HA | Late teens | Good CV; limited VF | None | 1. Cataract surgery |
| II-1 | F | 46 | 7 | Severe to profound | Oral; HA | 18 | Good CV; limited VF | Mild | 1. Cataract surgery |
LMG199 | II-1 | M | 49 | 33 | Mild to severe | Oral; HA | Teens | 20/40; can read; VF 5° OS, 15° OD | None | |
| II-2 | M | 56 | Teens | Moderate | Oral; HA | 11 | Can’t read; VF <5° | None | 1. MD and glaucoma OD 2. Cataract surgery |
LMG201 | II-2 | F | 26 | 18 | Moderate to severe | Oral; HA | 15 | Good CV; 20° VF | None | |
LMG202 | III-2 | F | 56 | 1–2 | Moderate to severe | Oral; HA | Early childhood | No useful vision | None | 1. Ichthyosis; affected brother has USH and ichthyosis |
LMG203 | IV-2 | F | 56 | >35 | Moderate to severe | Oral; HA | Early childhood | No useful vision | None | |
LMG206 | III-2 | F | 54 | 6 | Severe to profound | Sign + oral; HA | Early childhood | Can read large print; very limited VF | None | 1. Cataract surgery |
LMG214 | II-3 | F | 60 | 5 | Profound | Sign + oral; CI | 9 | 20/200; can read large print; VF <5° | None (normal) | 1. Cataract surgery |
| II-1 | F | 70 | Infancy | Profound | Sign + oral; no HA or CI | 17 | Light perception, gross objects | None | |