The outcome of cardiac intervention in patients with Williams syndrome (n=17)
| Heart defect | No | Age at intervention (median y, range) | Type of intervention | No | Follow up time (median y, range) | Outcome | (No) |
|---|---|---|---|---|---|---|---|
| SVAS | 7 | 11.0 (3.1–45) | Aortoplasty cum coretex patch | 5 | 9.7 (5–15) | No restennosis | (2) |
| Mild restenosis | (2) | ||||||
| Aortic valve insufficiency | (1) | ||||||
| Aortoplasty am Brom | 1 | 2 | Aortic valve insufficiency | (1) | |||
| Aortoplasty cum coretex patch, resection musculorum | 1 | 10 | Aortic valve insufficiency | (1) | |||
| SVAS+PAS | 2 | 1.7 (0.5–6.0) | MPA angioplasty | 1 | 8 | No result, recovery of PAS, SVAS followed | (1) |
| Aortoplasty cum coretex patch, reconstruction MPA, LPA, RPA cum coretex | 1 | 1 | LPA stenosis, aortic valve insufficiency | (1) | |||
| PAS | 3 | 0.8 (0.4–2.5) | Reconstruction MPA, LPA, RPA cum homograft, secclusio ASD, | 2 | 4 (3–8) | Mild restenosis | (2) |
| RPA angioplasty | 1 | 8 | No result, spontaneous recovery | (1) | |||
| SVAS+PAS+Coa+CMP | 4 | 0.2 (0.1–0.4) | Aortoplasty cum coretex, resection arcus ao distalis et anastomosis end to end, reconstruction MPA, LPA, RPA | 1 | 5 | Mild recoarctation | (1) |
| Reconstructio arcus ao cum subclavian flap, angioplasty arcus aortae postoperativa | 1 | 7 | Moderate recoarctation | (1) | |||
| Aortoplasty cum subclavian flap | 1 | 4 | Mild recoarctation and PAS | (1) | |||
| Angioplasty of PAS and SVAS | 1 | 13 | Moderate SVAS | (1) | |||
| Tetralogy of Fallot | 1 | 1.3 | Secclusio VSD, reconstruction MPA, LPA, RPA cum pericardial patch | 1 | 3 | Mild PAS | (1) |