Table 1

The import of peroxisome matrix proteins of fibroblasts from complementation group A (CG-A) patients

No		Type		Catalase			AOX			D bifunctional protein		PT
No		Type		37°C	30°C		37°C	30°C		37°C	30°C	37°C	30°C
A-06	ZS	0	10		10	100	0	0	0	10
A-02	ZS	0	0		0	60	0	0	0	0
A-14	ZS	0	0		0	50	0	0	0	0
A-10	ZS	0	5		10	60	0	0	0	5
A-05	NALD	0	90		0	100	5	60	5	80
A-08	NALD	0	80		0	90	0	50	0	80
A-04	IRD	0	60		0	80	0	50	0	70

Cells were cultured for 72 hours at either 37°C or 30°C and immunostained by antibodies of peroxisome matrix proteins. Immunopositive cells were defined as over 100 immunoreactive particles stained by each antibody in a cell. Immunopositive cells among 20 cells were counted in five view fields at a magnification ×1000 and data are averages of these in percentages.