Table 2

Clinical summary of 12 Usher II families

Family	Origin	HOMOG	Audiogram	RP DX (y)	RP symptoms	Enamel
735	English/USA	0.9969	Moderate-severe	30	Mild	—
1848	Irish/USA	0.9945	Moderate-severe	32	Mild	Normal
964	Swedish	0.9837	Moderate-severe	31	Mild	Normal
1121	German/USA	0.9187	Severe-profound	28	Mild-mod	Normal
1417	Dutch	0.9187	Moderate-severe	26	Moderate	Normal
2488	USA	0.8776	Severe-profound	32	Mild	Normal
1389	Dutch	0.7907	Moderate-severe	6	Moderate	Normal
736	English/USA	0.7779	Moderate-severe	30	Moderate	—
1372	Dutch	0.7392	Moderate-severe	15	Moderate	Normal
843	English/USA	0.7378	Severe-profound	5	Severe	Hypoplasia
49	Dutch/USA	0.0	Severe-profound	3	Severe	Hypoplasia
1322	USA	0.0	Severe-profound	17	Moderate	—

(—) denotes data not currently available.