Subject No | Sex/age (y) | Echocardiographic | Electrocardiographic | BP | |||||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|
IVS (mm) | PW (mm) | Area of hypertrophy | ASH | SAM | Abn rep | Inc volts | Abn Q waves | ↑Atria | LVH | ||||
1.II.2 | M/58 | 12 | 10 | Ivs + apex | y | n | y | n | n | n | n | 130/80 | |
1.II.3 | F/55 | 22 | 10 | Ivs | y | n | y | n | y | y | n | 140/80 | |
1.II.6 | F/53 | 9 | 8 | NA | n | n | n | n | n | n | n | 110/80 | |
1.II.8 | F/47 | 14 | 9 | Ivs | y | n | n | n | n | n | n | 150/90 | |
1.III.6 | M/34 | 36 | 13 | Ivs + pw | y | y | PM | PM | PM | PM | PM | 140/80 | |
1.III.8 | M/29 | 13 | 13 | Ivs + pw | n | n | y | n | n | n | n | 120/70 | |
1.III.10 | M/30 | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | |
1.III.11 | F/27 | 10 | 8 | NA | n | n | n | n | n | n | n | 110/70 | |
1.IV.2 | F/14 | 13 | 9 | Ivs | y | y | y | n | y | n | n | 100/50 | |
1.IV.6 | F/8 | 6 | 6 | NA | n | n | n | n | n | n | n | na | |
4.I.1 | F/70 | 8 | 8 | NA | NA | n | na | na | na | na | na | na | |
4.II.1 | M/48 | 24 | 12 | Ivs + pw | y | y | na | na | na | na | na | na | |
4.II.3 | M/na | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | |
4.II.6 | F/33 | 9 | 9 | NA | NA | n | n | n | n | n | n | 120/80 | |
4.III.1 | F/10 | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | |
10.I.1 | F/32 | 24 | 10 | Ivs | y | n | na | na | na | na | na | 100/70 | |
24.II.1 | M/56 | 28 | 16 | Ivs | y | y | y | y | n | n | n | 150/80 | |
24.III.2 | M/29 | 12 | 12 | Ivs + pw | NA | n | n | n | n | n | n | 130/80 | |
31.III.1 | M/52 | 10 | 10 | NA | n | n | y | n | n | n | n | 130/95 | |
31.III.4 | M/51 | 18 | 11 | Ivs + apex | y | n | y | n | n | n | n | 125/85 | |
31.III.6 | M/57 | 13 | 12 | Ivs + apex + pw | n | n | y | n | y | n | n | 160/110 | |
31.III.8 | M/54 | 13 | 12 | Ivs + apex + pw | n | n | y | n | y | y | y | 150/100 | |
31.IV.1 | M/20 | 10 | 10 | NA | n | n | y | n | n | n | n | 130/80 | |
31.IV.2 | M/18 | 9 | 10 | NA | n | n | n | n | n | n | n | 120/60 | |
31.IV.3 | M/15 | 7 | 7 | NA | NA | n | n | n | n | n | n | 120/75 | |
31.IV.4 | M/23 | 26 | 11 | Ivs + pw | n | y | y | n | n | n | y | 130/60 | |
31.IV.5 | M/22 | 23 | 8 | Ivs | n | y | n | n | n | n | n | 120/70 | |
31.IV.6 | M/19 | 40 | na | Ivs + apex | y | y | y | n | n | n | n | 110/70 | |
31.IV.8 | F/15 | 10 | 10 | NA | NA | n | n | n | n | n | n | 140/90 | |
31.IV.14 | M/27 | 9 | 9 | NA | n | n | n | n | n | n | n | 140/90 | |
38.II.1 | M/40 | na | na | na | na | na | n | n | n | n | n | na | |
38.II.3 | M/38 | 9 | 10 | NA | NA | n | y | y | n | n | n | 140/90 | |
38.II.4 | M/38 | 12.7 | 12.7 | Ivs + apex | n | n | y | y | n | n | n | 145/90 | |
38.II.6 | M/35 | na | na | na | na | na | n | n | n | n | n | na | |
38.III.1 | F/12 | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | NI | |
38.III.3 | F/13 | na | na | na | na | na | n | n | n | n | n | na | |
SB902 | F/27 | 221-150 | 131-150 | Ivs + pw | y | y | y | n | y | y | y | 110/60 | |
SB983 | F/62 | 161-150 | 161-150 | Ivs + pw | y | y | y | n | y | y | y | 140/70 | |
SB995 | M/49 | 25 | 15 | Ivs + pw | y | y | n | n | n | n | n | 140/85 |
Abn Q waves = abnormal Q waves, Abn rep = abnormal repolarisation, Age = age at diagnosis, ASH = asymmetrical septal hypertrophy, ↑Atria = enlarged atria, BP = blood pressure (mm Hg), Inc volts = increased voltages, IVS (mm) = maximum end diastolic interventricular septal thickness in mm, Ivs = interventricular septum, LVH = left ventricular hypertrophy by Romhilt and Este's criteria, PW (mm) = maximum end diastolic posterior wall thickness in mm, pw = posterior left ventricular free wall, SAM = systolic anterior motion of the mitral valve, y = feature present, n = feature absent, NA = not applicable, na = records not available, NI = not investigated clinically,
↵1-150 = post myectomy values. Subjects under 16 years old are underlined.