Table 1

Diagnostic criteria for NF2

Bilateral vestibular schwannomas OR family history of NF2 PLUS
 (1) Unilateral VS OR
(2) Any two of: meningioma, glioma, neurofibroma, schwannoma, posterior subcapsular lenticular opacities
Additional criteria
 Unilateral VS + any two of: meningioma, glioma, neurofibroma, schwannoma, and posterior subcapsular opacities
OR
Multiple meningioma (2 or more) + unilateral VS or any 2 of: glioma, neurofibroma, schwannoma, and cataract