Table 2

Four pairs of monozygotic twins with FAP-I

OriginIndonesia22 Sweden23 MajorcaPortugal
SexFemaleMaleMaleMale
Symptoms of FAP-IBothOnly oneBothBoth
Difference in onset age (y)4? (>7)124
Different clinical expression:YesNAYesYes
 in sensorimotor syndromeYesNAYesYes
 in digestive disturbancesYesNAYesYes
 in renal involvementYesNAYesNP
 in vitreous depositsNPNAYesNP
 in cardiac involvementYesNANPYes
Probability of monozygosityPresumedPresumed99.03%99.99%
  • NA=not applicable (only one affected); NP=not present in any.