Table 1

Frequency of transmission of the larger and smaller alleles at the Machado-Joseph disease locus

MeiosisAllele transmittedχ2assuming 1:1 segregationp (χ2)
LargerSmallerNot informativeTotal typed
MZ
 Paternal233118721.1580.276
 Maternal283221810.2670.606
DZ
 Paternal7580441990.1610.688
 Maternal7886552190.3900.532
Total
 Paternal98111622710.8090.368
 Maternal106118763000.6430.423